Quick Tips: Portopulmonary Hypertension

Our next LFN Quick Tips post is on another pulmonary complication of end-stage liver disease, portopulmonary hypertension.

Please make sure to check out our previous "Quick Tips" infographics:

Links to the referenced articles

Krowka MJ. Transplantation 2016 

Krowka MJ. Clin Liver Dis 2020

Kim WR et al. Liver Transpla 2000 - accuracy of Doppler echocardiography in assessing pulmonary hypertension

Galie N et al. Eur Heart J 2016

Rodriguez-Roisin R et al. Eur Respir J 2004

Savale L et al. Eur Respir J 2013 - efficacy of bosentan in PPHTN

Fisher JH et al. Eur Respir J 2015 - efficacy of PDE-5 inhibitors in PPHTN

Melgosa MT et al. Liver Transpl 2010 - efficacy of inhaled iloprost (prostacyclin analogue) in PPHTN

Ghofrani HA et al. NEJM 2013 - riociguat for treatment of pulmonary hypertension

AbuHalimeh B et al. Hepatology 2019